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Mycophenolate therapy in interstitial pneumonia with autoimmune features: a cohort study.


ABSTRACT:

Objectives

International experts recently characterized interstitial pneumonia with autoimmune features (IPAF) as a provisional diagnosis for patients with interstitial lung disease who have characteristics of autoimmune disease but do not meet criteria for a specific autoimmune disease. We describe clinical characteristics of IPAF patients and examine responses to mycophenolate as a therapy for IPAF.

Methods

This retrospective cohort included adult patients meeting European Respiratory Society/American Thoracic Society classification criteria for IPAF. Sociodemographic, clinical, and pulmonary function test data were abstracted for patients with and without mycophenolate treatment and followed longitudinally from interstitial lung disease diagnosis for change in pulmonary f

SUBMITTER: McCoy SS 

PROVIDER: S-EPMC6219314 | biostudies-literature | 2018

REPOSITORIES: biostudies-literature