Epidemiologic, Clinicopathologic, Diagnostic, and Management Challenges of Pityriasis Rubra Pilaris: A Case Series of 100 Patients.

ABSTRACT:

Importance

Pityriasis rubra pilaris (PRP) is a rare papulosquamous disorder with limited epidemiologic and clinicopathologic data. Little information is available on long-term outcomes, comorbidities, and treatment efficacy.

Objective

To evaluate objective and subjective disease experience metrics from the perspectives of patients and clinicians.

Design, setting, and participants

One hundred patients with a putative diagnosis of PRP and who elected to participate completed a comprehensive survey, followed by acquisition of their medical records, including histopathology slides and reports. The data were analyzed separately from the health care clinician and the patient perspectives. Two academic dermatologists examined clinical notes, pathology reports, and photograph

SUBMITTER: Ross NA 

PROVIDER: S-EPMC6262840 | biostudies-literature | 2016 Jun

REPOSITORIES: biostudies-literature