Dietary Management of Propionic Acidemia: Parent Caregiver Perspectives and Practices.

ABSTRACT:

Background

Propionic acidemia (PA), an autosomal recessive metabolic disorder, has an estimated incidence of 1:105,000-130,000 in the United States.^1,2 Nutrition management is a main intervention for PA. Research in inborn errors of metabolism such as phenylketonuria has identified association of parental perceptions and practices with dietary outcomes. Parental perceptions and practices in the nutrition management of PA have not been investigated.

Objective

To assess the dietary perceptions and practices of parental caregivers of children affected by PA.

Methods

PA parents were surveyed about perceptions and practices associated with feeding their affected child(ren). The single-page survey was anonymous, and responses to survey items were not identifiable

SUBMITTER: Lea D 

PROVIDER: S-EPMC6395508 | biostudies-literature | 2019 Mar

REPOSITORIES: biostudies-literature