QRS alternans due to localized intraventricular block during ventricular tachycardia in Uhl's anomaly: a case report.

ABSTRACT:

Background

Uhl's anomaly is a rare congenital heart disease characterized by 'Paper-like thinning of the right ventricular (RV) wall'. Since most patients with Uhl's anomaly die in infancy or childhood, the adult cases of this disorder have been limitedly reported and there were no past report describing this anomaly with ventricular tachycardia (VT), in which catheter ablation was successfully performed.

Case summary

We report the case of a 43-year-old man with a suggested Uhl's anomaly and VT. He underwent a catheter ablation of the recurrent VT. An electrophysiological study showed the VT (cycle length = 460 ms) with a right bundle branch block pattern and inferior axis represented QRS alternans. Concealed entrainment by pacing from the anterior right ventricle (RV) sugge

SUBMITTER: Nakasuka K 

PROVIDER: S-EPMC6439377 | biostudies-literature | 2019 Mar

REPOSITORIES: biostudies-literature