Long-term outcomes after intervention for pulmonary atresia with intact ventricular septum.

ABSTRACT:

Objective

Pulmonary atresia with intact ventricular septum (PA/IVS) can be treated by various operative and catheter-based interventions. We aim to understand the long-term transplant-free survival of patients with PA/IVS by treatment strategy.

Methods

Cohort study from the Pediatric Cardiac Care Consortium, a multi-institutional registry with prospectively acquired outcome data after linkage with the National Death Index and the Organ Procurement and Transplantation Network.

Results

Eligible patients underwent neonatal surgery or catheter-based intervention for PA/IVS between 1982 and 2003 (median follow-up of 16.7 years, IQR: 12.6-22.7). Over the study period, 616 patients with PA/IVS underwent one of three initial interventions: aortopulmonary shunt, right ventricu

SUBMITTER: Wright LK 

PROVIDER: S-EPMC6571047 | biostudies-literature | 2019 Jul

REPOSITORIES: biostudies-literature