An instrumented timed up and go in facioscapulohumeral muscular dystrophy.

ABSTRACT:

Introduction

Instrumenting timed functional motor tasks may reveal a continuum of motor disability that predicts future motor dysfunction.

Methods

We performed a prospective study of the instrumented timed up and go (iTUG) test in genetically confirmed facioscapulohumeral muscular dystrophy (FSHD) participants using a commercially available system of wireless motion sensors. Patients returned within 2 weeks to determine test-retest reliability. Gait parameters in FSHD participants were compared with a normative database, FSHD clinical severity score, manual muscle testing, and patient-reported functional disability.

Results

Gait parameters in FSHD participants were significantly (P < 0.05) altered compared with normative values, and reliability was excellent (intracla

SUBMITTER: Huisinga J 

PROVIDER: S-EPMC6631361 | biostudies-literature | 2018 Mar

REPOSITORIES: biostudies-literature