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Gerbode defect formation two decades after tetrology of fallot repair.

ABSTRACT: Although most intracardiac defects are congenital, a small fraction may be acquired during life. The Gerbode defect is an abnormal anatomical connection between the left ventricle and the right atrium. We describe herein a patient who initially underwent repair of tetralogy of Fallot (TOF). Years after TOF repair, he developed severe dyspnea. Extensive evaluation revealed that he had developed a Gerbode defect. Very few cases of acquired Gerbode defect have been previously reported. Management options are predominantly surgical interventions.

SUBMITTER: Ambesh P

PROVIDER: S-EPMC6639883 | biostudies-literature | 2019 Jul-Sep

REPOSITORIES: biostudies-literature

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Gerbode defect formation two decades after tetrology of fallot repair.

Ambesh Paurush P Hirsch Melissa M Tobin-Hess Aviva A Kazmi Danish D Kapoor Aditya A Shetty Vijay V Kamholz Stephan S

Annals of cardiac anaesthesia 20190701 3

Although most intracardiac defects are congenital, a small fraction may be acquired during life. The Gerbode defect is an abnormal anatomical connection between the left ventricle and the right atrium. We describe herein a patient who initially underwent repair of tetralogy of Fallot (TOF). Years after TOF repair, he developed severe dyspnea. Extensive evaluation revealed that he had developed a Gerbode defect. Very few cases of acquired Gerbode defect have been previously reported. Management o ...[more]

PMID: 31274502

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