Liver transplantation for severe portopulmonary hypertension: A case report and literature review.

ABSTRACT:

Background

Portopulmonary hypertension (PoPH) is not uncommon in patients waiting for liver transplantation (LT). Severe PoPH has a very high perioperative mortality rate and is still considered a contraindication for LT. Many patients with liver disease require but cannot receive LT due to severe PoPH and eventually died. We report a patient with severe PoPH who underwent successful LT and had near normal pulmonary pressure without drug treatment.

Case summary

A 39-year-old woman was hospitalized with the chief complaint of jaundice and exertional dyspnea and fatigue. Caroli disease and liver cirrhosis was diagnosed 6 years previously. Her liver disease met the criteria for LT. However, right heart catheterization showed that her mean pulmonary artery pressure was increased

SUBMITTER: Chen XJ 

PROVIDER: S-EPMC6854406 | biostudies-literature | 2019 Nov

REPOSITORIES: biostudies-literature