Diagnosis and management of congenital absence of pericardium: a case report.

ABSTRACT:

Background

Absence of the pericardium is a rare congenital defect with an approximate incidence of <1/10 000. We review a case of complete pericardial agenesis in a symptomatic patient with gross cardiac mobility, for which pericardial reconstruction was undertaken successfully.

Case summary

A 24-year-old otherwise fit and well patient, with debilitating exertional chest pain was found to have complete pericardial agenesis on the left side and on the diaphragmatic surface. There was gross cardiac mobility demonstrated on cardiac magnetic resonance imaging. His pericardium was reconstructed surgically using Gore-tex^® patches. There were no complications, and the patient was discharged 8 days later. Three months later at follow-up, the patient required no analgesia

SUBMITTER: Bouchard M 

PROVIDER: S-EPMC6939816 | biostudies-literature | 2019 Dec

REPOSITORIES: biostudies-literature