Ventriculoatrial malalignment in atrioventricular septal defect resulting in uniatrial biventricular connection: surgical options.

ABSTRACT:

Background

Uniatrial biventricular connection (UBC) is a rare cardiovascular anomaly characterized by absence of one atrioventricular connection and drainage of the other atrium via a solitary atrioventricular valve into both ventricles. The absent atrioventricular connection may affect either the left or right atrium. Because of the absence of one atrioventricular connection hearts with UBC have been classified among functionally univentricular hearts requiring palliative treatment according to the Fontan principle.

Aims/objective

We report two further patients with UBC. In one of these patients careful echocardiographic examination of the atrioventricular junction in early infancy revealed the possibility of biventricular repair based on the favorable anatomy of the atriov

SUBMITTER: Hofbeck M 

PROVIDER: S-EPMC7161119 | biostudies-literature | 2020 Apr

REPOSITORIES: biostudies-literature