The French paediatric cohort of Castleman disease: a retrospective report of 23 patients.

ABSTRACT:

Background

Castleman disease (CD) is a rare non-malignant lymphoproliferation of undetermined origin. Two major disease phenotypes can be distinguished: unicentric CD (UCD) and multicentric CD (MCD). Diagnosis confirmation is based on histopathological findings in a lymph node. We attempted to survey all cases of paediatric CD identified to date in France to set up a national registry aiming to improve CD early recognition, treatment and follow-up, within the context of a new national reference center (http://www.castleman.fr).

Methods

In 2016, we e-mailed a questionnaire to members of the French paediatric immunohaematology society, the paediatric rheumatology society and the Reference Centre for Castleman Disease to retrospectively collect cases of paediatric CD (first sym

SUBMITTER: Borocco C 

PROVIDER: S-EPMC7164260 | biostudies-literature | 2020 Apr

REPOSITORIES: biostudies-literature