A case report of capillary leak syndrome with recurrent pericardial and pleural effusions.

ABSTRACT:

Background

Capillary leak syndrome (CLS) is a rare connective tissue disease, triggered by the leak of serous fluid into the interstitial spaces, characterized by a hallmark of oedema and effusions in confined spaces. The limiting factor in CLS management appears to be its diagnosis rather than treatment, which is usually to contain the disease progression rather than a cure.

Case summary

We report a case of a 51-year-old woman with recurrent life-threatening presentations of pericardial effusions, pleural effusions, and generalized swelling of face and extremities. The only notable past medical history was of Type 1 diabetes. Numerous investigations did not lead to specific disease accounting for pericardial effusions and pleural effusions. Eventually, the diagnosis of CLS

SUBMITTER: Khan HR 

PROVIDER: S-EPMC7180544 | biostudies-literature | 2020 Apr

REPOSITORIES: biostudies-literature