Simplified Diet for nutrition management of phenylketonuria: A survey of U.S. metabolic dietitians.

ABSTRACT:

Background

Phenylketonuria (PKU) is an inherited metabolic disorder affecting the conversion of phenylalanine (Phe) to tyrosine. Medical nutrition therapy, consisting of a Phe-restricted diet with medical formula, is the primary treatment for PKU. The Simplified Diet is an approach to PKU nutrition management that allows certain fruits, vegetables, and low-protein foods to be eaten without measuring or tracking, referred to as free/uncounted foods. There is no consensus on how to implement this approach in metabolic centers in the United States (U.S.), and clinical practice varies.

Aim

This study describes the clinical experience of metabolic dietitians in U.S.-based metabolic centers related to the use and implementation of the Simplified Diet.

Methods

A survey was d

SUBMITTER: Hansen J 

PROVIDER: S-EPMC7203646 | biostudies-literature | 2020 May

REPOSITORIES: biostudies-literature