Surgical management of non-syndromic ectopia lentis.

ABSTRACT:

Aim

To compare whether aphakic contact lenses or secondary iris-claw intraocular lenses are superior in the refractive management post-pars plana vitreolensectomy in a pedigree with an FBN1 mutation causing non-syndromic ectopia lentis (NSEL) with retinal detachment (RD).

Methods

Eight affected individuals had pars plana vitreolensectomy for bilateral ectopia lentis (EL). Twelve eyes of 6 patients had secondary iris-claw intraocular lenses inserted and 4 eyes of 2 patients were managed with contact lenses. Rhegmatogenous retinal detachment (RRD) was treated when necessary. Pre- and post-operative assessment included visual acuity, endothelial cell count and dilated fundal examination.

Results

Macula-on RRD was present in all individuals >18y, 64% (7/11 eyes) pr

SUBMITTER: Stephenson KA 

PROVIDER: S-EPMC7321954 | biostudies-literature | 2020

REPOSITORIES: biostudies-literature