Outcomes in adults with congenital heart disease and heterotaxy syndrome: A single-center experience.

ABSTRACT:

Background

Heterotaxy syndrome (HS) is a condition in which the thoracoabdominal organs demonstrate an abnormal lateral arrangement and is often associated with congenital heart disease (CHD). Little is known about the adult HS population with CHD.

Objective

To describe the outcomes and sociodemographics of the adult CHD population with HS.

Methods

Records of patients 18 years of age or older with diagnoses of both CHD and HS at Texas Children's Hospital from 1964 to 2018 were reviewed.

Results

Sixty-two patients met inclusion criteria. Median age was 22.7 [IQR 19.6-30.0] years; 26 (42%) were female; and 13 (21%) of patients had a gap in care of >3 years. Median follow-up time in adulthood was 2.9 [IQR 1.3-8.2] years. Forty-three (69%) of patients had single ve

SUBMITTER: Broda CR 

PROVIDER: S-EPMC7376960 | biostudies-literature | 2019 Nov

REPOSITORIES: biostudies-literature