Left heart matters in Ebstein's anomaly: the importance of a closer follow up-a case report.

ABSTRACT:

Background

Ebstein's anomaly (EA) is mainly thought of as a right heart condition, however, congenital left-sided lesions can co-exist. Therefore, it is paramount to include the left side of the heart as part of a routine investigation in these patients. We present a 57-year-old symptomatic patient with EA and progressive tricuspid regurgitation (TR) associated with acquired left ventricular outflow obstruction (LVOTO).

Case summary

A 57-year-old women, known to have severe EA presented with shortness of breath and chest pain on exertion secondary to progression of the tricuspid valve regurgitation and right ventricle dilatation leading to a dynamic compression of the left outflow tract requiring surgical intervention.

Discussion

Left ventricular obstruction secondary

SUBMITTER: Ordonez MV 

PROVIDER: S-EPMC7501933 | biostudies-literature | 2020 Aug

REPOSITORIES: biostudies-literature