Dataset Information
Anomalous origin of coronary arteries from pulmonary artery in adults: a case series.
Ontology highlight
ABSTRACT: Background
Anomalous origin of a coronary artery from the pulmonary trunk is a small group of rare congenital anomalies present in up to 1% of the population. These patients, in absence of an adequate collateral supply, may present with congestive heart failure secondary to ischaemia, arrhythmia, or sudden cardiac death in up to 90% of cases within the first months of life.Case summary
We present four cases diagnosed in adulthood over 10 years in two high-volume centres. The first patient presented with dyspnoea and orthopnoea. The second with chest pain and episodes of non-sustained ventricular tachycardia. The third patient presented during her third pregnancy with chest pain, palpitations, and arrhythmia (non-sustained ventricular tachycardia). The fourth patient presented with sudden cardiac death.Discussion
In all cases with anomalous origin of coronary arteries, it is recommendable to consider surgical correction to avoid the progression of ischaemia, congestive heart failure, arrhythmia, and sudden death.
SUBMITTER: Vergara-Uzcategui CE
PROVIDER: S-EPMC7534175 | biostudies-literature | 2020 Jun
REPOSITORIES: biostudies-literature
Publications
Anomalous origin of coronary arteries from pulmonary artery in adults: a case series.
European heart journal. Case reports 20200312 2
<h4>Background</h4>Anomalous origin of a coronary artery from the pulmonary trunk is a small group of rare congenital anomalies present in up to 1% of the population. These patients, in absence of an adequate collateral supply, may present with congestive heart failure secondary to ischaemia, arrhythmia, or sudden cardiac death in up to 90% of cases within the first months of life.<h4>Case summary</h4>We present four cases diagnosed in adulthood over 10 years in two high-volume centres. The firs ...[more]