Focused Update on Pulmonary Hypertension in Children-Selected Topics of Interest for the Adult Cardiologist.

ABSTRACT: Pulmonary hypertensive vascular disease (PHVD), and pulmonary hypertension (PH), which is a broader term, are severe conditions associated with high morbidity and mortality at all ages. Treatment guidelines in childhood are widely adopted from adult data and experience, though big differences may exist regarding aetiology, concomitant conditions and presentation. Over the past few years, paediatric aspects have been incorporated into the common guidelines, which currently address both children and adults with pulmonary hypertension (PH). There are multiple facets of PH in the context of cardiac conditions in childhood. Apart from Eisenmenger syndrome (ES), the broad spectrum of congenital heart disease (CHD) comprises PH in failing Fontan physiology, as well as segmental PH. In this review

SUBMITTER: Albinni S 

PROVIDER: S-EPMC7559541 | biostudies-literature | 2020 Aug

REPOSITORIES: biostudies-literature