Adolescent Kawasaki disease shock syndrome with inflammatory cell infiltration into the myocardium: a case report.

ABSTRACT:

Background

Kawasaki disease (KD) is a self-limiting form of systemic vasculitis. KD usually occurs in infants and young children and is rarely seen in adolescents. On rare occasions, KD is accompanied with reduced organ perfusion due to systolic hypotension, a condition known as Kawasaki disease shock syndrome (KDSS). The multifactorial causes of KDSS may include intensive vasculitis with capillary leak, myocardial dysfunction, and release of proinflammatory cytokines. However, the mechanisms underlying the pathophysiology of KDSS have not been fully elucidated.

Case summary

A febrile 17-year-old male with cervical lymphadenopathy developed extreme shock with rapid cardiac dysfunction and reduced organ perfusion. Electrocardiogram revealed ST elevation in the precordial lead

SUBMITTER: Sugiura Y 

PROVIDER: S-EPMC7649480 | biostudies-literature | 2020 Oct

REPOSITORIES: biostudies-literature