IgG4 related disease as a cause of isolated retroperitoneal fibrosis with no other organ involvement; Case report.

ABSTRACT:

Introduction and importance

Retroperitoneal fibrosis (RPF) is a rare disease characterized by the replacement of normal tissue with fibrosis and inflammation. We present the case of a 40-years-old gentleman with RPF whose presenting complaints were bilateral flank pain and weight loss and was found to have IgG4 related disease. To the best of our knowledge, IgG4-related disease with isolated retroperitoneal involvement is a very rare occurrence.

Case presentation

The diagnosis of IgG4-Related retroperitoneal fibrosis was made based on clinical, radiological and histopathological criteria. Imaging revealed isolated retroperitoneal involvement and the patient was started on oral steroids with a good clinical response after ten days. Repeated imaging months later showed signifi

SUBMITTER: Razok A 

PROVIDER: S-EPMC7773681 | biostudies-literature | 2021 Jan

REPOSITORIES: biostudies-literature