Adherence to best practice consensus guidelines for familial Mediterranean fever: a modified Delphi study among paediatric rheumatologists in Turkey.

ABSTRACT:

Background

Although not validated fully, recommendations are present for diagnosis, screening and treatment modalities of patients with familial Mediterranean fever (FMF).

Objective

To review the current practices of clinicians regarding FMF and reveal their adherence to consensus guidelines.

Methods

Fifteen key points selected regarding the diagnosis and management of FMF were assessed by 14 paediatric rheumatologists with a three-round modified Delphi panel.

Results

Consensus was reached on the following aspects: genetic analysis should be ordered to all patients when clinical findings support FMF, but its result is not decisive alone. In the absence of clinical features, colchicine should be commenced when two pathogenic alleles and family history of amyloid

SUBMITTER: Kavrul Kayaalp G 

PROVIDER: S-EPMC7811395 | biostudies-literature | 2022 Jan

REPOSITORIES: biostudies-literature