Potts anastomosis in children with severe pulmonary arterial hypertension and atrial septal defect.

ABSTRACT:

Aims

Potts shunt has been proposed as a bridge or alternative to lung transplantation for children with severe and drug-refractory suprasystemic pulmonary arterial hypertension (PAH). We describe the management of the atrial shunt when a Potts shunt is planned in refractory PAH.

Methods and results

We report a case series of children in whom a Potts shunt was done for severe PAH associated with an atrial septal defect to illustrate the different clinical and haemodynamic scenarios. Five children (2 to 13 years) underwent a Potts shunt: three surgical, one percutaneous Potts shunt, and one percutaneous stenting of a restrictive arterial duct. All had associated atrial septal defect. Those who had generalized cyanosis before the procedure had a complicated postoperative course

SUBMITTER: Capel A 

PROVIDER: S-EPMC7835613 | biostudies-literature | 2021 Feb

REPOSITORIES: biostudies-literature