Elevated Ambulatory Blood Pressure Measurements are Associated with a Progressive Form of Fabry Disease.

ABSTRACT:  INTRODUCTION: Published data on hypertension incidence and management in Anderson-Fabry disease are scant and the contribution of elevated blood pressure to organ damage is not well recognized.

Aim

Therefore, we have assessed blood pressure values and their possible correlations with clinical findings in a well described cohort of Fabry patients.

Methods

Between January 2015 and May 2019, all adult Fabry patients (n = 24 females, n = 8 males) referred to our institute were prospectively enrolled. During the first examination patient's genotype and clinical characteristics were recorded. Blood pressure data were obtained by standard observed office measurements followed, within 6 months, by ambulatory blood pressure monitoring and home self-recordings. Organ involvement, incl

SUBMITTER: Rossi F 

PROVIDER: S-EPMC8087548 | biostudies-literature | 2021 May

REPOSITORIES: biostudies-literature