Project description:A 32-year-old woman with a history of mild congenital pulmonic stenosis presented with new dyspnea on exertion. Multimodal imaging revealed a quadricuspid pulmonic valve with supravalvular ridge. We illustrate the evaluation and diagnosis of this rare condition. (Level of Difficulty: Advanced.).

| S-EPMC8299973 | biostudies-literature

Bicuspid Pulmonic Valve and Pulmonary Artery Aneurysm.

Project description:Bicuspid pulmonary valves and pulmonary artery aneurysms are two rare entities, reported in association, and usually attributed to hemodynamic alterations caused by the bicuspid pulmonary valve. We present magnetic resonance images of a patient with a bicuspid pulmonary valve and pulmonary artery aneurysm, and propose an alternative mechanism for this association, based on recent embryologic studies that link anomalies of the semilunar valves and great vessels with derangement of the cardiac neural crest cell development.

| S-EPMC4505617 | biostudies-literature

Quadricuspid pulmonary valve and left pulmonary artery aneurysm in an asymptomatic patient assessed by cardiovascular MRI.

Project description:We present a coincidental finding of quadricuspid pulmonary valve and left pulmonary artery aneurysm. As both the pulmonary valve and the pulmonary trunk with its main branches are hard to visualise with cardiac ultrasound, most abnormalities described so far are from autopsy series. With the increasing use of CMR and its excellent potential for visualising both pulmonary valve and pulmonary arteries, we believe more cases will be discovered in the near future. Although pulmonary artery aneurysm are rare, timely detection may prevent lethal bleeding.

| S-EPMC3673605 | biostudies-literature

Mechanical pulmonic valve thrombosis: expanding role of cardiac CT and multimodality imaging.

Project description:We report a case of a 44-year-old man with a clinical history of Tetralogy of Fallot status post staged surgical correction with mechanical pulmonic valve replacement who presented with progressive exertional dyspnea in the setting of non-compliance with anticoagulation. In the context of this suggestive clinical presentation, the diagnosis of mechanical pulmonic valve thrombosis (MPVT) was made possible via multimodality imaging, including transthoracic echocardiogram and cardiac computed tomography angiography. Due to the uncommon nature of the condition, the patient was treated with systemic thrombolysis and anticoagulation using evidence-based guidelines, largely extrapolated from left-sided mechanical valve thrombosis. Our case underscores the importance of anticoagulation in MPVT and recognizing the features of MPVT on clinical history, physical examination, and multimodality imaging. It is essential to understand the pivotal role of multimodality imaging in the assessment of MPVT and realize the limitations of available data regarding the management of MPVT in the current era.

| S-EPMC9270197 | biostudies-literature

Quadricuspid Pulmonary Valve: Case Report and the Comparison with Quadricuspid Aortic Valve.

Project description:BackgroundQuadricuspid pulmonary valve (QPV) is a rare congenital anomaly. Simple QPV had been mainly diagnosed at the time of autopsy before 2000, and the frequency rates of QPV are approximately 0.02%-0.41%. QPV was initially diagnosed using transthoracic echocardiography (TTE) after 2000 and with contrast computed tomography (CT) or cardiac magnetic resonance imaging (CMR) after 2009. Obtaining the cross-sectional view of the pulmonary valve using TTE is difficult. We aimed to review the papers regarding the incidence, embryology, diagnosis, associated congenital heart anomalies, and prognosis in patients with QPV, and furthermore to compare with those in patients with quadricuspid aortic valve (QAV).Case presentationWe diagnosed QPV with mild stenosis in a 12-month-old infant. With a slight angulation of the transducer superiorly from the left high parasternal short-axis view, a short-axis view of QPV was obtained.ResultsIn QPV cases diagnosed at autopsy, Hurwitz's type-b with three equal cusps and one smaller cusp is dominant, whereas Hurwitz's type-a with four equal cusps is dominant in clinically diagnosed cases. Congenital heart anomaly and valvular stenosis are more frequent in patients with QPV than in patients with QAV. Coronary artery anomalies and infectious endocarditis are more frequent in patients with QAV than in patients with QPV. The incidence of PR is more common in type-a QPV than in type-b QPV. There is no difference between type-a QAV and type-b QAV with respect to the incidence of aortic regurgitation (AR). It is assumed that QPV is a risk factor for a Ross operation. However, QPVs have been used as autografts in certain patients.ConclusionBetween QPV and QAV, various differences were found in frequency rates, diagnostic methods, valve morphology, valve function, associated congenital heart diseases, and frequencies of infectious endocarditis.

| S-EPMC10201900 | biostudies-literature

A giant coronary aneurysm with a coronary artery-pulmonary artery fistula: 14 years of follow-up with multimodality imaging.

Project description: Not available

| S-EPMC9487894 | biostudies-literature

Multimodality imaging of isolated bicuspid pulmonary valve leading to pulmonary stenosis.

Project description: Not available

| S-EPMC5337025 | biostudies-literature

Multimodality Imaging of Anomalous Left Coronary Artery from the Pulmonary Artery.

Project description: Not available

| S-EPMC5658291 | biostudies-literature

Multimodality Imaging of a Giant Circumflex Coronary Artery Aneurysm in a Septuagenarian.

Project description: Not available