Palliative care in pulmonary hypertension associated with congenital heart disease: systematic review and expert opinion.

ABSTRACT:

Aims

Pulmonary arterial hypertension (PAH) is common amongst patients with congenital heart disease (CHD). It is a severe and complex condition that adversely affects quality of life and prognosis. While quality of life questionnaires are routinely used in clinical pulmonary hypertension practice, little is known on how to interpret their results and manage PAH-CHD patients with evidence of impaired health-related quality of life, especially those with advanced disease and palliative care needs.

Methods and results

We performed a systematic review of studies concerning palliative care for people with PAH-CHD, also reviewing the health-related quality of life literature pertaining to these patients. Of 330 papers identified through initial screening, 17 were selected for incl

SUBMITTER: Constantine A 

PROVIDER: S-EPMC8120400 | biostudies-literature | 2021 Jun

REPOSITORIES: biostudies-literature