Clinical experience with the treatment of retroperitoneal vascular leiomyosarcoma originating from large veins.

ABSTRACT:

Background

Retroperitoneal vascular leiomyosarcoma (RVLMS) is an extremely rare disease in clinical practice, and it has poor prognosis. This article is to explore the diagnosis and treatment of RVLMS and present our experience.

Methods

Data of RVLMS patients were continuously collected in our hospital from August 2018 to February 2020: two males and two females with a median age of 56 (min-max = 33-61) years were included. Patients in whom paraganglioma could not be excluded were asked to take phenoxybenzamine before surgery. A multi-disciplinary team (MDT) meeting had been held and surgery was recommended. The operation procedures varied based on the tumor location, shape, and stage, and the core steps were "exposure of the retroperitoneum and tumor, identification of vita

SUBMITTER: Zhang HX 

PROVIDER: S-EPMC8364698 | biostudies-literature | 2021 Aug

REPOSITORIES: biostudies-literature