Adaptation and Validation of a Questionnaire to Evaluate Knowledge of the Low Phe Diet in PKU.
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ABSTRACT:
SUBMITTER: Ramos-Alvarez R
PROVIDER: S-EPMC8400675 | biostudies-literature | 2021 Aug
REPOSITORIES: biostudies-literature
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Adaptation and Validation of a Questionnaire to Evaluate Knowledge of the Low Phe Diet in PKU.
Ramos-Álvarez Rodolfo R Kapp Maili M Rodríguez-Ruiz María Mercedes MM Fausor Rocío R Bueno-Delgado María Amor MA Ahring Kirsten K Waisbren Susan E SE
Nutrients 20210807 8
Phenylketonuria (PKU) is an autosomal recessive disorder of phenylalanine (Phe) metabolism, causing a build-up of Phe in the body. Treatment consists of a Phe-restricted diet for life and regular determination of blood Phe levels to monitor the intake of Phe. Despite the fact that diet is the cornerstone of treatment, there are no studies examining common knowledge about food items and whether they are allowed as part of the PKU diet. Improving parents' and patients' knowledge and competence abo ...[more]
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