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Novel transcatheter treatment for staged closure of Abernethy malformation with portal hypoplasia.

ABSTRACT: Portosystemic shunts are rare congenital malformations that come to attention due to various hepatic and extrahepatic manifestations. Management of this malformation is dictated by the presence and adequacy of intrahepatic portal radicals. Staged occlusion of the shunt is recommended in patients with severely hypoplastic portal radicals. We describe a novel transcatheter technique that we improvised for staged occlusion of Abernethy malformation in a 2-year-old girl.

SUBMITTER: Sasikumar D

PROVIDER: S-EPMC8457293 | biostudies-literature | 2021 Jul-Sep

REPOSITORIES: biostudies-literature

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Novel transcatheter treatment for staged closure of Abernethy malformation with portal hypoplasia.

Sasikumar Deepa D Valakkada Jineesh J Kramadhari Harshith H Ayyappan Anoop A Krishnamoorthy Kavasseri M KM

Annals of pediatric cardiology 20210701 3

Portosystemic shunts are rare congenital malformations that come to attention due to various hepatic and extrahepatic manifestations. Management of this malformation is dictated by the presence and adequacy of intrahepatic portal radicals. Staged occlusion of the shunt is recommended in patients with severely hypoplastic portal radicals. We describe a novel transcatheter technique that we improvised for staged occlusion of Abernethy malformation in a 2-year-old girl. ...[more]

PMID: 34667420

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