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Primary Epicardial Malt Lymphoma: A New Physiopathologic Entity Mimicking a Pericardial Compressive Syndrome.


ABSTRACT: MALT lymphoma is a non-Hodgkin lymphoma developing from B cells and is a type of marginal zone lymphoma. It can develop in any organs, but no case of primary cardiac location has yet been reported. We report the first observation of a primary epicardial MALT lymphoma mimicking a compressive pericardial syndrome. (Level of Difficulty: Advanced.).

SUBMITTER: Grandmougin D 

PROVIDER: S-EPMC8572141 | biostudies-literature | 2021 Nov

REPOSITORIES: biostudies-literature

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Primary Epicardial Malt Lymphoma: A New Physiopathologic Entity Mimicking a Pericardial Compressive Syndrome.

Grandmougin Daniel D   Bouhlel Mahmoud Cheikh MC   Lardenois Emilie E   Donaint Pierre P   Benigni Paolo P   Sbaffi Alessandra A   Sirbu Christina C   Feugier Pierre P   Touati Rabea R   Maureira Juan-Pablo JP  

JACC. Case reports 20211103 15


MALT lymphoma is a non-Hodgkin lymphoma developing from B cells and is a type of marginal zone lymphoma. It can develop in any organs, but no case of primary cardiac location has yet been reported. We report the first observation of a primary epicardial MALT lymphoma mimicking a compressive pericardial syndrome. (<b>Level of Difficulty: Advanced.</b>). ...[more]

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