Radiological pleuroparenchymal fibroelastosis-like lesion in idiopathic interstitial pneumonias.

ABSTRACT:

Background

Pleuroparenchymal fibroelastosis (PPFE) is characterised by predominant upper lobe pleural and subpleural lung parenchymal fibrosis. Radiological PPFE-like lesion has been associated with various types of interstitial lung diseases. However, the prevalence and clinical significance of radiological PPFE-like lesion in patients with idiopathic interstitial pneumonias (IIPs) are not fully understood. We aimed to determine the prevalence and clinical impact on survival of radiological PPFE-like lesion in patients with IIPs.

Methods

A post-hoc analysis was conducted using data from the Japanese nationwide cloud-based database of patients with IIPs. All the patients in the database were diagnosed as having IIPs by multidisciplinary discussion. Patients diagnosed with id

SUBMITTER: Fujisawa T 

PROVIDER: S-EPMC8582158 | biostudies-literature | 2021 Nov

REPOSITORIES: biostudies-literature