Thirty-Year Survival after Cardiac Surgery for Patients with Turner Syndrome.

ABSTRACT:

Objective

To evaluate long-term survival in patients with Turner syndrome after congenital heart surgery with a focus on left heart obstructive lesions (LHOLs).

Study design

We queried the Pediatric Cardiac Care Consortium, a US-based registry of congenital heart surgery, for patients with Turner syndrome undergoing congenital heart surgery at <21 years of age between 1982 and 2011. Outcomes were obtained from the Pediatric Cardiac Care Consortium and from national death and transplant registries through 2019. Survival of patients with Turner syndrome and nonsyndromic patients with similar LHOL was compared by Kaplan-Meier survival curves and Cox regression adjusted for age, congenital heart disease, and era.

Results

We identified 179 patients with Turner syndrome ope

SUBMITTER: Alam S 

PROVIDER: S-EPMC8626205 | biostudies-literature | 2021 Dec

REPOSITORIES: biostudies-literature