A case report of primary cardiac intimal sarcoma presenting with atrial fibrillation and a left atrial mass.

ABSTRACT:

Background

Intimal sarcoma is an exceedingly rare type of primary cardiac tumour. It is characterized by poorly differentiated spindle-shaped cells that can mimic smooth muscle and is strongly associated with MDM2 genetic amplification. Owing to its rarity and non-distinctive histological features, diagnosis remains a significant challenge.

Case summary

In this case report, we describe a case of primary cardiac intimal sarcoma in a 37-year-old woman who presented with atrial fibrillation (AF) and a left atrial mass. Despite having a histological sample from an excised left atrial mass, the diagnosis was not made until she presented with back pain secondary to metastatic disease to the spine.

Discussion

Primary cardiac intimal sarcoma is an extremely rare diagnosis. Th

SUBMITTER: Ho K 

PROVIDER: S-EPMC8633751 | biostudies-literature | 2021 Nov

REPOSITORIES: biostudies-literature