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Heart Failure in a Child: Multimodality Approach Leading to an Unusual Cause.


ABSTRACT: Heart failure secondary to isolated pulmonary artery vasculitis is rarely described in children. We describe a 10-year-old child who presented with right heart failure symptoms, severe pulmonary hypertension, and bilateral branch pulmonary artery stenosis secondary to isolated pulmonary artery vasculitis. (Level of Difficulty: Advanced.).

SUBMITTER: Karuru UD 

PROVIDER: S-EPMC8642737 | biostudies-literature | 2021 Dec

REPOSITORIES: biostudies-literature

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Heart Failure in a Child: Multimodality Approach Leading to an Unusual Cause.

Karuru Uma Devi UD   Relan Jay J   Verma Mansi M   Kumar Sanjeev S   Tripathi Madhavi M   Gupta Saurabh Kumar SK   Ramakrishnan Sivasubramanian S   Saxena Anita A   Kothari Shyam S SS  

JACC. Case reports 20211201 17


Heart failure secondary to isolated pulmonary artery vasculitis is rarely described in children. We describe a 10-year-old child who presented with right heart failure symptoms, severe pulmonary hypertension, and bilateral branch pulmonary artery stenosis secondary to isolated pulmonary artery vasculitis. (<b>Level of Difficulty: Advanced.</b>). ...[more]

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