Case report of the broad spectrum of late complications in an adult patient with univentricular physiology palliated by the Fontan circulation.

ABSTRACT:

Background

At the most severe end of the spectrum of congenital heart disease are patients with an univentricular physiology. They comprise a heterogeneous group of congenital heart malformations that have the common characteristic that the cardiac morphology is not equipped for sustaining a biventricular circulation.

Case summary

Here, we present a case of an adult patient after Fontan palliation, illustrative of the complex clinical course and the broad spectrum of complications that can be encountered during follow-up, highlighting the need for a multidisciplinary approach in the clinical care for these patients.

Discussion

During the surgical Fontan procedure, the inferior vena cava is connected to the pulmonary circulation, after prior connection of the superior

SUBMITTER: Nederend M 

PROVIDER: S-EPMC8867817 | biostudies-literature | 2022 Feb

REPOSITORIES: biostudies-literature