When dystrophia meets ischaemia: a case report on cardiac involvement of myotonic dystrophy type 2 and successful arrhythmia elimination after catheter ablation.

ABSTRACT:

Background

This case reviews the cardiac involvement of myotonic dystrophy type 2 in terms of ventricular arrhythmias (VAs) and individual myocardial scar formation as target for catheter ablation.

Case summary

A 62-year-old woman with myotonic dystrophy type 2 and a severely reduced left ventricular ejection fraction (25%) presented with recurrent episodes of VAs and consecutive implantable cardioverter-defibrillator therapies. The patient already underwent two VA ablation attempts focusing on an ischaemia-related arrhythmia substrate in the left ventricle. The patient was scheduled for repeat ablation after the progression of coronary artery disease was ruled out. Interestingly bipolar voltage as well as activation mapping revealed an arrhythmia substrate along with the ba

SUBMITTER: Guckel D 

PROVIDER: S-EPMC8874836 | biostudies-literature | 2022 Feb

REPOSITORIES: biostudies-literature