Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension.

ABSTRACT:

Background

Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group.

Case presentation

Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension.

Conclusions

Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options.

SUBMITTER: Rabiee P 

PROVIDER: S-EPMC9050997 | biostudies-literature | 2022 Apr

REPOSITORIES: biostudies-literature