Incidence Rate and Prevalence of Systemic Sclerosis and Systemic Sclerosis-Associated Interstitial Lung Disease in Japan: Analysis Using Japanese Claims Databases.

ABSTRACT:

Introduction

Systemic sclerosis (SSc) is a complex autoimmune disease with increased mortality, and interstitial lung disease (ILD) is a major cause of death. There are no recent epidemiological data on SSc and SSc-associated ILD (SSc-ILD) in Japan and little is known about how patients with these diseases are treated.

Methods

The incidence rate and prevalence of SSc and SSc-ILD in Japan were estimated using the Japanese Medical Data Centre (JMDC) database. The demographic and clinical characteristics of patients and the immunomodulatory medications they received were also assessed using JMDC and the Medical Data Vision (MDV) databases. All analyses were descriptive.

Results

The overall incidence rates of SSc and SSc-ILD per 100,000 person-years were 6.6 (95% confiden

SUBMITTER: Kuwana M 

PROVIDER: S-EPMC9056456 | biostudies-literature | 2022 May

REPOSITORIES: biostudies-literature