Extensive Aortic Thromboembolism in a Patient With Erdheim-Chester Disease: A Case Report.

ABSTRACT:

Background

Erdheim-Chester disease (ECD) is a rare disease that affects multiple systems and is characterized by non-Langerhans cell histiocytosis. Classic clinical signs include long bone infiltration, central nervous system involvement, diabetes insipidus, and sheathing of the entire aorta. However, thrombosis is not recognized as a typical cardiac manifestation of ECD. Here, we report the case of an ECD patient with extensive arterial thrombus formation and embolism in several sections of the aorta.

Case

A 36-year-old woman was admitted due to recurrent fever and left finger cyanosis for 20 days. Laboratory tests revealed that her C-reactive protein and interleukin-6 levels were significantly elevated. Thoracic computed tomographic angiography (CTA) revealed thrombosis fr

SUBMITTER: He J 

PROVIDER: S-EPMC9139267 | biostudies-literature | 2022

REPOSITORIES: biostudies-literature