Coronary artery aneurysm in Loeys-Dietz syndrome: a case report.

ABSTRACT:

Background

Loeys-Dietz syndrome (LDS) is a connective tissue disorder that commonly presents with vascular abnormalities. Owing to the rarity and severity of the condition, consensus guidelines for aortic surgery thresholds vary. In addition, evaluation of coronary arteries in patients with LDS (either routinely or before aortic root surgery) remain undefined. In this case report, we discuss a patient with LDS who found to have an ectatic aortic root and a coronary artery aneurysm and discuss guidelines for evaluation and management in this patient population.

Case summary

A 48-year-old woman was incidentally found to have a 45 mm ectatic aortic root during evaluation for a neck mass. As part of pre-operative evaluation for aortic root replacement, left heart catheterization

SUBMITTER: Jost ZT 

PROVIDER: S-EPMC9161713 | biostudies-literature | 2022 Jun

REPOSITORIES: biostudies-literature