Low-grade fibromyxoid sarcoma in the middle ear as a rare location: a case report.

ABSTRACT:

Background

Low-grade fibromyxoid sarcoma (LGFMS) is a rare soft tissue tumor with a misleadingly bland histological appearance and fully malignant behavior, typically occurring in the deep soft tissues of the proximal extremities or trunk of young adults. However, no cases of primary middle ear LGFMS have been reported previously. LGFMS is characterized by high rates of local recurrence and metastatic spread, which should be attached of great importance to clinical diagnosis and treatment.

Case description

Herein, we report an unusual case of LGFMS occurring primarily in the middle ear of a 12-year-old boy, who presented with aural fullness and gradually progressive hearing loss in the left ear for 6 months, without other related symptoms and family history. Preoperative ima

SUBMITTER: Guo Y 

PROVIDER: S-EPMC9253951 | biostudies-literature | 2022 Jun

REPOSITORIES: biostudies-literature