The association of ectopic craniopharyngioma in the fourth ventricle with familial adenomatous polyposis: illustrative case.

ABSTRACT:

Background

Craniopharyngioma (CP) often arises in the sellar and suprasellar areas; ectopic CP in the posterior fossa is rare. Familial adenomatous polyposis (FAP) is a genetic disorder involving the formation of numerous adenomatous polyps in the gastrointestinal tract, and it is associated with other extraintestinal manifestations.

Observations

The authors reported the case of a 63-year-old woman with FAP who presented with headache and harbored a growing mass in the fourth ventricle. Magnetic resonance imaging (MRI) findings revealed a well-circumscribed mass with high intensity on T1-weighted images and low intensity on T2-weighted images and exhibited no contrast enhancement. Gross total resection was performed and histopathology revealed an adamantinomatous CP (aCP). T

SUBMITTER: Uemura H 

PROVIDER: S-EPMC9379701 | biostudies-literature | 2022 Jan

REPOSITORIES: biostudies-literature