Strategy of delayed repair of total anomalous pulmonary venous connection in right atrial isomerism and functional single ventricle.

ABSTRACT:

Objective

Repair of total anomalous pulmonary venous connection (TAPVC) in neonates with right atrial isomerism and functional single ventricle is challenging. In our novel strategy, primary draining vein stenting (DVS) was applied to patients with preoperative pulmonary vein obstruction to delay TAPVC repair. This study investigated our initial experience with a strategy of delayed TAPVC repair, incorporating DVS.

Methods

Twenty-nine patients with right atrial isomerism and functional single ventricle who had a severe obstruction in the course of draining veins, who required surgical or catheter intervention in their neonatal period were retrospectively reviewed (primary DVS: n = 11; primary TAPVC repair: n = 18).

Results

Patients in the primary DVS group had more mi

SUBMITTER: Kisamori E 

PROVIDER: S-EPMC9390631 | biostudies-literature | 2022 Jun

REPOSITORIES: biostudies-literature