Biventricular Assist Device Support for Intractable Arrhythmias From Histiocytoid Cardiomyopathy.

ABSTRACT: Histiocytoid cardiomyopathy (HICMP) is a rare mitochondrial cardiomyopathy associated with recurrent life-threatening arrhythmias and variable degrees of systolic dysfunction. Successful heart transplantation for HICMP has been described, but there has been no published experience with biventricular assist device (BiVAD) support for intractable arrhythmias in HICMP. We report a 13 month old girl with left ventricular noncompaction and preserved systolic function who presented in cardiogenic shock secondary to incessant ventricular arrhythmias. After failed attempts at chemical and electrical cardioversion, she underwent BiVAD implantation as bridge to transplantation. Her BiVAD course was complicated by mechanical inflow obstruction during sinus rhythm, necessitating left-sided cannulation

SUBMITTER: Magnetta DA 

PROVIDER: S-EPMC9568621 | biostudies-literature | 2022 Nov

REPOSITORIES: biostudies-literature