The epidemiology of rare types of hepatobiliary and pancreatic cancer from national cancer registry.

ABSTRACT:

Background

Information on rare hepatobiliary and pancreatic (HBP) subtypes of cancer is scarce. We aimed to elucidate the incidence and clinical features of rare tumors in Japan using the National Cancer Registry (NCR), a new nationwide integrated population-based registry.

Methods

The data of patients diagnosed in 2016-2017 were extracted from the NCR database, and classified by topography: liver cells, intrahepatic bile duct, gallbladder, extrahepatic bile duct, ampulla of Vater, and pancreas. Data were described and analyzed using the World Health Organization and General Rules tumor classifications. The incidences for all rare tumors including hepatoblastoma and adenosquamous cell carcinoma were calculated as the number of new cases divided by the corresponding total per

SUBMITTER: Satake T 

PROVIDER: S-EPMC9596567 | biostudies-literature | 2022 Nov

REPOSITORIES: biostudies-literature