Successful laparoscopic pheochromocytoma resection in an adult patient with Fontan physiology: a case report.

ABSTRACT:

Background

Pheochromocytoma is a rare tumour producing catecholamines and has been more frequently reported than expected in patients with a Fontan physiology.

Case summary

The patient was a 39-year-old woman born with a univentricular atrioventricular connection and pulmonary valve stenosis. A Fontan operation was performed when she was 22 years old. At the age of 38, she was diagnosed with pheochromocytoma. The most serious problem was the increased occurrence of supraventricular arrhythmias, which easily caused heart failure. We decided to perform a laparoscopic resection. Postoperative recovery was good. There were no findings of malignancy and all postoperative catecholamine levels normalized. She was discharged home on the 14th day after the surgery, walking unaided.

SUBMITTER: Nohara-Shitama Y 

PROVIDER: S-EPMC9648512 | biostudies-literature | 2022 Nov

REPOSITORIES: biostudies-literature