Successful management of Stanford type A aortic dissection with severe scoliosis in the setting of Marfan syndrome: a case report.

ABSTRACT:

Background

Marfan syndrome (MFS) is a connective tissue disorder involving multiple organs. The most severe complications include aortic root dilatation and dissection. In the present report, we provide an uncommon case of acute aortic Stanford type A dissection (AADA) repair with severe scoliosis in an MFS patient and it is even more rare for such surgical treatment to be successfully completed along with holistic management that enables the patient to recover successfully. We offer a reference for future surgical therapy since the specific surgical treatment methods in this case have not been reported in the literature.

Case description

A 40-year-old Chinese female with MFS was rushed to our surgical clinic due to the sudden onset of intense chest pain. Physical examinatio

SUBMITTER: Huang S 

PROVIDER: S-EPMC9652535 | biostudies-literature | 2022 Oct

REPOSITORIES: biostudies-literature