Curative Pericardiectomy in Interpheron-Resistant Severe Pericardial Erdheim-Chester Disease.

ABSTRACT: Erdheim-Chester disease is a rare clonal non-Langerhans cell histiocytosis with multisystemic involvement. It affects bones, large vessels, and retroperitoneum. Cardiac involvement is one of the main mortality predictors.¹ We present an unusual case that debuted with cardiac tamponade and pericardial constriction requiring pericardiectomy for definitive control. (Level of Difficulty: Intermediate.).

SUBMITTER: Gomez-Herrero J 

PROVIDER: S-EPMC9700060 | biostudies-literature | 2022 Nov

REPOSITORIES: biostudies-literature