Adult-onset Still's disease in Western Australia: Epidemiology, comorbidity and long-term outcome.

ABSTRACT:

Aim

Adult-onset Still's disease (ASD) is a rare, potentially life-threatening autoinflammatory condition. As reported prevalence shows regional variation and long-term outcome data are scarce, we investigated epidemiology and long-term health outcomes of ASD in Western Australia (WA).

Methods

Population-based cohort study using longitudinally linked administrative health data from all WA hospitals between 1999 and 2013 for ASD patients (ICD-10-AM M06.1) and controls matched for age, gender, and index year. Rate ratios and odds ratios (RR/OR) with 95% confidence intervals (CI) compared ASD patients with controls.

Results

The average ASD incidence (n = 52) was 0.22/100 000 with 2.4/100 000 point-prevalence as of December 31, 2013. ASD patients (median age 41.5 years, 59

SUBMITTER: Nossent J 

PROVIDER: S-EPMC9805040 | biostudies-literature | 2022 Nov

REPOSITORIES: biostudies-literature