Undifferentiated embryonic sarcoma of the adult liver with paraneoplastic syndrome: a case report.

ABSTRACT:

Background

Undifferentiated embryonic sarcoma of the liver (UESL) is a rare primary liver sarcoma that mainly affects children. Since it was first reported in 1978, less than 100 cases of UESL in adults have been reported. Due to the lack of specificity of clinical symptoms and imaging findings, the misdiagnosis rate of UESL is very high, and the definite diagnosis is usually in the late stage. Paraneoplastic syndrome (PNS) is a clinical symptom caused by the production of hormones or hormone-like substances in some tumors. This report describes the clinical diagnosis and treatment of patients with these 2 rare disorders. The imaging, histological, and genetic manifestations of UESL are described. This study provides support for the clinical research progress of UESL.

Case descr

SUBMITTER: Luan T 

PROVIDER: S-EPMC9834581 | biostudies-literature | 2022 Dec

REPOSITORIES: biostudies-literature