Pulmonary veno-occlusive disease in Sjogren's syndrome: a case report.

ABSTRACT:

Background

Pulmonary arterial hypertension (PAH) associated with connective tissue disease (CTD) belongs to Group 1 pulmonary hypertension. Pulmonary veno-occlusive disease (PVOD), which is characterized by venous system aberrations, has been previously reported in CTD-PAH; however, it has rarely been observed in Sjogren's syndrome (SS).

Case presentation

Our 28-year-old female patient was admitted to the hospital with recurrent shortness of breath even after minimal physical activity. Her chest high-resolution CT scan demonstrated pulmonary artery dilatation and bilateral ground-glass nodules. A subsequent right heart catheterization confirmed pulmonary hypertension because her mean pulmonary arterial pressure was 62 mmHg. Our inquisitive genomic assessment identified a nov

SUBMITTER: Zeng X 

PROVIDER: S-EPMC9847112 | biostudies-literature | 2023 Jan

REPOSITORIES: biostudies-literature